Tatalaksana Medis Protein-Losing Enteropathy Pasca Bedah Total Cavo Pulmonary Connection
Abstract
Sebelum bedah Fontan diperkenalkan, penyakit jantung bawaan (PJB) kompleks yang tidak ideal untuk reparasi biventrikular dilakukan bedah paliatif pulmonar y ar ter y banding (PAB)atau systemic-to-pulmonary shunt. PAB adalah upaya untuk memperkecil lumen ar teri pulmonal sehingga alirannya berkurang, dengan memasang ikatan melingkari arteri pulmonal cabang utama.Sedangkan bedah systemic-to-pulmonar y shunt adalah memasang saluran penghubung antara cabang cranial aorta ke arteri pulmonal. Tetapi harapan hidup pasen-pasen ini hanya berlangsung dua hingga tiga dekade saja.
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References
Giannaco S, Hammad F, Amodeo A, Michielon G, Drago F, Turchetta A, et al. Clinical outcome of 193 extracardiac Fontan patients: The first 15 years. J Am Coll Cardiol 2006;47:2065-73.
Driscoll DJ, Offord KP, Feldt RH, Schaff HV, Puga FJ, Danielson GK. Five-to fifteen-year follow-up after Fontan operation. Circulation 1992;85:469-496.
Fontan F, Kirklin JW, Fernandez G, Costa F, Naftel DC, Tritto F, et al. Outcome after a “perfect” Fontan operation. Circulation 1990;81:1520-36.
Webb GD, Smallhorn JF, Therrien J, Redington AN: Congenital Heart Diseases. In Braunwauld Heart Disease. 7th ed. Philadelphia, Elsevier Saunders, 2005.
Mertens L, Hagler DJ, Sauer U, Somerville J, Gewillig M. Protein-losing enteropathy after the Fontan operation: An international multicenter study. J Thorac Cardiovasc Surg 1998;115:1063-73.
Bernstein D, Naftel D, Chin C, Addonizio LJ, Gamberg P, Blume ED, et al. Outcome of listing for cardiac transplantation for failed Fontan: A multi-institutional study. Circulation 2006;114:273-80.
Binder HJ: Disorders of Absorption. In Harrison’s Principles of Internal Medicine. 16th ed. New York, McGraw-Hill, 2005.
Ostrow AM, Freeze H, Rychik J. Protein-losing enteropathy after Fontan operation: Investigations into possible patho-physiologic mechanisms. Ann Thorac Surg 2006;82:695-700.
Rychik J. Pathogenesis and current management options for protein-losing enteropathy. 56th Annual Scientific Session ACC 2007. March 24-27, 2007 New Orleans.
Rychik J, Spray TL. Strategies to treat protein-losing enteropathy. Semin Thorac Cardiovasc Surg Pediatr Card Surg Annu 2002;5:3-11.
Murch SH, Winyard PJ, Koletzko S, Wehner B, Cheema HA, Risdon RA, et al. A congenital enterocyte heparin sulfate deficiency with massive albumin loss, secretory diarrhea, and malnutrition. Lancet 1996;347:1299-1301.
Bode L, Eklund EA, Murch S, Freeze HH. Heparan sulfate depletion amplifies TNF-á-induced protein leakage in an in vitro model of protein-losing enteropathy. Am J Physiol Gastrointest Liver Physiol 2005;288:G1015-23.
Lin W, Hwang M, Chung H, Chu J, Lai M, Yang J, et al. Protein-losing enteropathy after the Fontan operation: Clinical analysis of nine cases. Chang Gung Med J 2006;29:505-12.
Rychik J, Rome JJ, Jacobs ML. Late surgical fenestration for complications after the Fontan operation. Circulation 1997;96:33-6.
Cohen MI, Rhodes LA, Wernovsky G, Gaynor JW, Spray TL, Rychik J. Atrial pacing: an alternative treatment for protein-losing enteropathy after the Fontan operation. J Thorac Cardiovasc Surg 2001;121:582-3.
Kelly AM, Feldt RH, Driscoll DJ, Danielson GK. Use of heparin in the treatment of protein-losing enteropathy after Fontan operation for complex congenital heart disease. Mayo Clin Proc 1998;73:777-9.
Uzun O, Wong JK, Bhole V, Stumper O. Resolution of protein-losing enteropathy and normalization of mesenteric doppler flow with Sildenafil after Fontan. Ann Thorac Surg 2006;82:e39-e40.
Jayakumar KA, Addonizio LJ, Kichuk-Chrisant MR, Galantowicz ME, Lamour JM, Quaegebeur JM, et al. Cardiac transplantation after the Fontan or Glenn Procedure. J Am Coll Cardiol 2004;44:2065-72.
Driscoll DJ, Offord KP, Feldt RH, Schaff HV, Puga FJ, Danielson GK. Five-to fifteen-year follow-up after Fontan operation. Circulation 1992;85:469-496.
Fontan F, Kirklin JW, Fernandez G, Costa F, Naftel DC, Tritto F, et al. Outcome after a “perfect” Fontan operation. Circulation 1990;81:1520-36.
Webb GD, Smallhorn JF, Therrien J, Redington AN: Congenital Heart Diseases. In Braunwauld Heart Disease. 7th ed. Philadelphia, Elsevier Saunders, 2005.
Mertens L, Hagler DJ, Sauer U, Somerville J, Gewillig M. Protein-losing enteropathy after the Fontan operation: An international multicenter study. J Thorac Cardiovasc Surg 1998;115:1063-73.
Bernstein D, Naftel D, Chin C, Addonizio LJ, Gamberg P, Blume ED, et al. Outcome of listing for cardiac transplantation for failed Fontan: A multi-institutional study. Circulation 2006;114:273-80.
Binder HJ: Disorders of Absorption. In Harrison’s Principles of Internal Medicine. 16th ed. New York, McGraw-Hill, 2005.
Ostrow AM, Freeze H, Rychik J. Protein-losing enteropathy after Fontan operation: Investigations into possible patho-physiologic mechanisms. Ann Thorac Surg 2006;82:695-700.
Rychik J. Pathogenesis and current management options for protein-losing enteropathy. 56th Annual Scientific Session ACC 2007. March 24-27, 2007 New Orleans.
Rychik J, Spray TL. Strategies to treat protein-losing enteropathy. Semin Thorac Cardiovasc Surg Pediatr Card Surg Annu 2002;5:3-11.
Murch SH, Winyard PJ, Koletzko S, Wehner B, Cheema HA, Risdon RA, et al. A congenital enterocyte heparin sulfate deficiency with massive albumin loss, secretory diarrhea, and malnutrition. Lancet 1996;347:1299-1301.
Bode L, Eklund EA, Murch S, Freeze HH. Heparan sulfate depletion amplifies TNF-á-induced protein leakage in an in vitro model of protein-losing enteropathy. Am J Physiol Gastrointest Liver Physiol 2005;288:G1015-23.
Lin W, Hwang M, Chung H, Chu J, Lai M, Yang J, et al. Protein-losing enteropathy after the Fontan operation: Clinical analysis of nine cases. Chang Gung Med J 2006;29:505-12.
Rychik J, Rome JJ, Jacobs ML. Late surgical fenestration for complications after the Fontan operation. Circulation 1997;96:33-6.
Cohen MI, Rhodes LA, Wernovsky G, Gaynor JW, Spray TL, Rychik J. Atrial pacing: an alternative treatment for protein-losing enteropathy after the Fontan operation. J Thorac Cardiovasc Surg 2001;121:582-3.
Kelly AM, Feldt RH, Driscoll DJ, Danielson GK. Use of heparin in the treatment of protein-losing enteropathy after Fontan operation for complex congenital heart disease. Mayo Clin Proc 1998;73:777-9.
Uzun O, Wong JK, Bhole V, Stumper O. Resolution of protein-losing enteropathy and normalization of mesenteric doppler flow with Sildenafil after Fontan. Ann Thorac Surg 2006;82:e39-e40.
Jayakumar KA, Addonizio LJ, Kichuk-Chrisant MR, Galantowicz ME, Lamour JM, Quaegebeur JM, et al. Cardiac transplantation after the Fontan or Glenn Procedure. J Am Coll Cardiol 2004;44:2065-72.
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How to Cite
Hidayat, S., Rahajoe, A., & Iskandarsyah, K. (1). Tatalaksana Medis Protein-Losing Enteropathy Pasca Bedah Total Cavo Pulmonary Connection. Indonesian Journal of Cardiology, 28(5), 364-369. https://doi.org/10.30701/ijc.v28i5.222
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